How to treat an extensive form of primary intestinal lymphangiectasia?

查看全文 作　　者：Rosana [1]Troskot;Dragan [1]Jurcic;Ante [1]Bilic;Marija Gomercic [2,3]Palcic;Stanko [4]Tezak;Ivana [5]Brajkovic

机构地区：[1]Faculty of Medicine,J.J.Strossmayer University of Osijek,Division of Gastroenterology and Hepatology,Department of Internal Medicine,Clinical Hospital“Sveti Duh”;[2]Division of Gastroenterology and Hepatology,Department of Internal Medicine,“Sestre milosrdnice”University Hospital Center;[3]University of Zagreb School of Medicine;[4]Clinical Department of Nuclear Medicine and Radiation Protection,University Hospital Centre Zagreb;[5]Dialysis clinic,Polyclinic“Sveti Duh”II

出　　处：《World Journal of Gastroenterology》索引2015年第21卷第23期,共6页

摘　　要：We report a case of a 42-year-old man with a rare disorder known as primary intestinal lymphangiectasia,which is characterized by dilated intestinal lymphatics that lead to the development of protein-losing enteropathy. The patient presented with a grand mal seizure caused by malabsorption-derived electrolytes and a protein disorder. Signs of the disease, including chronic diarrhea and peripheral edema, manifested10 years ago, but a diagnosis was never made. The diagnosis was suspected because of the clinical manifestations, laboratory tests, imaging and endoscopic findings. Hyperemic and edematous mucosa of the small intestine corresponded to scattered white spots with dilated intestinal lymphatics and whitish villi in the histological specimen of the biopsied jejunal mucosa.Although numerous therapeutic strategies are available,only octreotide therapy proved to be an effective means of therapeutic resolution in this patient. Although the patient had a partial remission following the use of a slow release formula of octreotide, his prognosis, clinical course, and future treatment challenges are yet to be determined. 关键词：PRIMARY INTESTINAL lymphangiec

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How to treat an extensive form of primary intestinal lymphangiectasia?

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