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199篇 您的检索式：作者名="Hoffmann J G"

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	题名	作者	年代	出处	被引量
1	Differential diagnosis in patients with suspected bile acid synthesis defects显示文摘AIM: To investigate the clinical presentations associated with bile acid synthesis defects and to describe identification of individual disorders and diagnostic pitfalls. METHODS: We describe semiquantitative determination of 16 urinary bile acid metabolites by electrospray ionization-tandem mass spectrometry. Sample preparation was performed by solid-phase extraction. The total analysis time was 2 min per sample. We determined bile acid metabolites in 363 patients with suspected defects in bile acid metabolism. RESULTS: Abnormal bile acid metabolites were found in 36 patients. Two patients had bile acid synthesis defects but presented with atypical presentations. In 2 other patients who were later shown to be affected by biliary atresia and cystic fibrosis the profile of bile acid metabolites was initially suggestive of a bile acid synthesis defect. Three adult patients suffered from cerebrotendinous xanthomatosis. Nineteen patients had peroxisomal disorders, and 10 patients had cholestatic hepatopathy of other cause. CONCLUSION: Screening for urinary cholanoids should be done in every infant with cholestatic hepatopathy as well as in children with progressive neurological disease to provide specific therapy.	Dorothea Haas Hongying Gan-Schreier Claus-Dieter Langhans Tilman Rohrer Guido Engelmann Maura Heverin David W Russell Peter T Clayton Georg F Hoffmann Jürgen G Okun	2012	World Journal of Gastroenterology2012，18，10：	2
2	Whole-genome duplications spurred the functional diversification of the globin gene superfamily in vertebrates 显示文摘	Hoffmann F G Opazo J C Storz J F	2012	Molecular Biology and Evolution2012，29，1：	1
3	Strategy and realization for introduction for the protection decision model (' IPS WEIZEN MODEL') against fungal diseases of wheat in the farming practice 显示文摘	Habermeyer J Hoffmann G M	1994	Zeitsehrift-fur-Pflanzenkrankheiten-und-Pflanzenschutz1994，101，6：	1
4	显示文摘	Li J T Hoffmann M W G Shen H	2012	J Mater Chem2012，22，20：	1
5	Air pollution and lung cancer incidence in 17 European cohorts: prospective analyses from the European Study of Cohorts for Air Pollution Effects (ESCAPE) 显示文摘	Raaschou-Nielsen 0 Andersen ZJ Beelen R Samoli E Stafoggia M Weinmayr G Hoffmann B Fischer P Nieuwenhuijsen MJ Brunekreef B Xun WW Katsouyanni K Dimakopoulou K Sommar J Forsberg B Modig L Oudin A Oftedal B Schwarze PE Nafstad p De Faire U Pedersen NL Ostenson CG Fratiglioni L Penell J Korek M Pershagen G Eriksen KT Serensen M Tjenneland A Ellermann T Eeftens M Peeters PH Meliefste K Wang M Bueno-de-Mesquita B Key TJ de Hoogh K Concin H Nagel G Yilier A Grioni S Krogh y Tsai MY Ricceri F Sacerdote C Galassi C Migliore E Ranzi A Cesaroni G Badaloni C Forastiere F Tamayo I Amiano P Dorronsoro M Trichopoulou A Bamia C Yineis p Hoek G	2013	Lancet Oncol2013，14，9：	1
6	Emission of the odor substances from fertilizer industry 显示文摘	Hoffmann J Gryglewicz G Hoffmann K	2009	Polish Journal of Chemical Technology2009，11，1：	1
7	Linking long-termdietary patterns with gut microbial enterotypes 显示文摘	Wu G D Chen J Hoffmann C	2011	Science2011，334，6052：	1
8	Pericardial fat, visceral abdominal fat, cardiovascular disease risk factors, and vascular calci- fication in a community-based sample: the Framingham Heart Study 显示文摘	Rosito G A Massaro J M Hoffmann U	2008	Circulation2008，117，5：	1
9	Annual cost of illness and quality-adjusted life year losses in the United States due to 14 foodborne pathogens显示文摘	HOFFMANN S BATZ M B MORRJS J J G	2012	Journal of Food Protection2012，75，7：	1
10	An X-ray absorption fine structure study of copper(I) chloride coordination structure in water up to 325 ℃ 显示文摘	Fulton J L Hoffmann M Darab J G	2000	Chem Phys Lett2000，330，：	1
11	Relationship of an-drogenic activity to body fat topography,fat cell morphology,andmetabolic aberrations in premenopausal women显示文摘	Evans D J Hoffmann R G Kalkhoff R K	1983	J Clin EndocrinolMetab1983，57，2：	1
12	Strategy and realization of introduction for the protection decision model ( 'IPS WEIZEN MODEL' ) against fungal diseases of wheat in the fanning practice 显示文摘	Haberm E J Hoffmann G M	1994	Zeitschrift - fur - Pflanzenschutz1994，101，：	1
13	Mobile sensor network control using mutual information methods and particle filters 显示文摘	G M Hoffmann C J Tomlin	2010	IEEE Transactions on Automatic Control2010，55，1：	1
14	Experimental study on combustion in porous media with a reciprocating flow system 显示文摘	Hoffmann J G Echigo R Yoshida H	1997	Combustion and Flame1997，111，：	1
15	Copper(I) and Copper(II) coordination structure under hydrothermal conditions at 325 ℃ : An X-ray absorption fine structure and molecular dynamics study 显示文摘	Fulton J L Hoffmann M M Darab J G Palmer B J	2000	J Phys Chem A2000，104，11：	1
16	Induction of inducible nitric oxide synthase expression by neopterin in vascular smooth muscle cells显示文摘	Schobersberger W Hoffmann G Grote J	1995	FEBS Lett1995，377，：	1
17	Decline in CD4+cell numbers in cats with naturally acquired feline immunodeficiency virus infection显示文摘	Hoffmann G Thum J Ackley C	1992	Journal of Virology1992，66，3：	1
18	Experimental study on combustion in porous media with a reciprocating flow system 显示文摘	HOFFMANN J G ECHIGO R YOSHIDA H	1997	Combustand Flame1997，111，12：	1
19	Structure features of a water-soluble pentosan in rye grain显示文摘	Hoffmann R A Kamerling J P Vliegenthart J F G	1992	Carbo Research1992，226，：	1
20	Streptococcus mutans and Streptococcus sobrinus biofilm formation and metabolic activity on dental materials显示文摘	Hahnel S Muhlbauer G Hoffmann J	2012	Acta Odontol Scand2012，70，2：	1

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