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| 1 | Properties of TiAICrN coatings prepared by vacuum cathodic arc ion plating显示文摘TiAlCrN 涂层在 TC11 (Ti-6.5Al-3.5Mo-1.5Zr-0.3Si ) 钛合金底层上借助于真空 cathodic 弧离子 plating 技术被扔。氮化物涂层的作文,阶段结构,机械表演,和氧化抵抗被扫描电子调查显微镜学(SEM ) ,原子力量显微镜(AFM ) , X 光检查衍射(XRD ) ,钻电子光谱学(AES ) ,和 X 光检查光电子显微镜学(XPS ) 。为准备钛合金的保护的涂层的一个新过程成功地被获得。试验性的结果显示在 TiAlN 涂层的增加的元素铬做贡献形成(220 ) 比较喜欢方向。涂层的阶段由组成(Ti,艾尔) N 并且(Ti, Cr ) N。在 700 琠敨 ? 佩 ? 敷敲眠汥? 牣獹慴汬穩摥椠 ? 桴 ? 整牴条湯污猠牴 ' | RU Qiang HU Shejun HUANG Nacan ZHAO Lingzhi QIU Xiuli HU Xianqi | 2008 | Rare Metals2008，27，3： | 9 |
| 2 | Exome sequencing reveals genetic architecture in patients with isolated or syndromic short stature显示文摘Short stature is among the most common endocrinological disease phenotypes of childhood and may occur as an isolated finding or in conjunction with other clinical manifestations.Although the diagnostic utility of clinical genetic testing in short stature has been implicated,the genetic architecture and the utility of genomic studies such as exome sequencing(ES)in a sizable cohort of patients with short stature have not been investigated systematically.In this study,we recruited 561 individuals with short stature from two centers in China during a 4-year period.We performed ES for all patients and available parents.All patients were retrospectively divided into two groups:an isolated short stature group(group I,n=257)and an apparently syndromic short stature group(group II,n=304).Causal variants were identified in 135 of 561(24.1%)patients.In group I,29 of 257(11.3%)of the patients were solved by variants in 24 genes.In group II,106 of 304(34.9%)patients were solved by variants in 57 genes.Genes involved in fundamental cellularprocess played an important role in the genetic architecture of syndromic short stature.Distinct genetic architectures and pathophysiological processes underlie isolated and syndromic short stature. | Xin Fan Sen Zhao Chenxi Yu Di Wu Zihui Yan Lijun Fan Yanning Song Yi Wang Chuan Li Yue Ming Baoheng Gui Yuchen Niu Xiaoxin Li Xinzhuang Yang Shiyu Luo Qiang Zhang Xiuli Zhao Hui Pan Mei Li Weibo Xia Guixing Qiu Pengfei Liu Shuyang Zhang Jianguo Zhang Zhihong Wu James R.Lupski Jennifer E.Posey Shaoke Chen Chunxiu Gong Nan Wu | 2021 | Journal of Genetics and Genomics2021，48，5： | 2 |
| 3 | Preliminary study on polymorphism analysis of SpRunt-lgene by PCR-SSCP in Strongylocentrotus interraedius and its association with growth traits 显示文摘 | Wang Xiuli Qiu Xuemei Meng Xiangying | 2010 | Molecular Biology Reports2010，37，1： | 1 |
| 4 | Preliminary study on polymorphism analysis of SpRunt-1 gene by PCR-SSCP in Strongylocentrotus intermedius and its association with growth traits显示文摘 | Wang Xiuli Qiu Xuemei Meng Xiangying | 2010 | Molecular Biology Reports2010，37，1： | 1 |
| 5 | Quasi‑Solid Electrolyte Interphase Boosting Charge and Mass Transfer for Dendrite‑Free Zinc Battery显示文摘The practical applications of zinc metal batteries are plagued by the dendritic propagation of its metal anodes due to the limited transfer rate of charge and mass at the electrode/electrolyte interphase.To enhance the reversibility of Zn metal,a quasi-solid interphase composed by defective metal-organic framework(MOF)nanoparticles(D-UiO-66)and two kinds of zinc salts electrolytes is fabricated on the Zn surface served as a zinc ions reservoir.Particularly,anions in the aqueous electrolytes could be spontaneously anchored onto the Lewis acidic sites in defective MOF channels.With the synergistic effect between the MOF channels and the anchored anions,Zn^(2+)transport is prompted significantly.Simultaneously,such quasi-solid interphase boost charge and mass transfer of Zn^(2+),leading to a high zinc transference number,good ionic conductivity,and high Zn^(2+)concentration near the anode,which mitigates Zn dendrite growth obviously.Encouragingly,unprecedented average coulombic efficiency of 99.8%is achieved in the Zn||Cu cell with the proposed quasi-solid interphase.The cycling performance of D-UiO-66@Zn||MnO_(2)(~92.9%capacity retention after 2000 cycles)and D-UiO-66@Zn||NH_(4)V_(4)O_(10)(~84.0%capacity retention after 800 cycles)prove the feasibility of the quasi-solid interphase. | Xueer Xu Yifei Xu Jingtong Zhang Yu Zhong Zhongxu Li Huayu Qiu Hao Bin Wu Jie Wang Xiuli Wang Changdong Gu Jiangping Tu | 2023 | Nano-Micro Letters2023，15，4： | 0 |
| 6 | Clinical research of biphenotypic acute leukemia witht(8;21)(q22;q22)显示文摘Objective:To report 4 cases of biphenotypic acute leukemia(BAL)with t(8;21)(q22;q22),and analyze the characteristics of morphology,immune phenotype,chromosome karyotype(MIC)and clinical manifestations.Methods:The BAL patients with t(8;21)(q22;q22)(group A)were compared with the randomly selected BAL patients with other clonical chromo- somal changes(group B)and acute myeloid leukemia M2 cases with t(8;21)(q22;q22)(group C)in MIC and clinical features. Results:BAL with t(8;21)(q22;q22)showed acute myeloid leukemia with high percentages of blast cells morphologically; revealed co-positive to B-lymphoid and myeloid lineages,frequent and high expressions of CD34 and CD33;were responsive to chemotherapy for myeloid and lymphocytic leukemia simultaneously well.Conclusion:A new subset of BAL with t(8;21)(q22;q22)was reported,and this suggests that the leukemia colony with t(8;21)(q22;q22)might originate from early phase of hematopoiesis. | Guangsheng He Ling Zhou Depei Wu Yongquan Xue Mingqing Zhu Jianying Liang Aining Sun Zhengming Jin Huiying Qiu Miao Miao Xiaowen Tang Zhengzheng Fu Xiao Ma Xiuli Wang | 2007 | The Chinese-German Journal of Clinical Oncology2007，6，4： | 0 |
| 7 | Anovel BRF1mutation intwomiddle-aged siblingswith cerebellofaciodental syndrome显示文摘To the Editor:Cerebellar-facial-dental syndrome(CFDS)is a rareand autosomal recessive(AR)neurodevelopmental disease,characterized by cerebellar hypoplasia and intellectual disability,facial dysmorphisms,short stature,microcephaly,and dental anomalies.ll'in 20is,Borck et observed threepairs of siblings with apreviously undescribed pattern of abnormalities andestablished CFD's as a clinicalentity,To date,a total of six CFDS families have been reported.li'4iThe age of the reported patients ranges from infancy to early adulthood.Since the rarity of CFDS,more study is requiredforevaluatingits natural historyand clinical characteristics.This paper would liketo report a novel homozygous BRF1 gene mutation in two middleaged CFDS patients from Chinese,and to summarize its clinical and genetic characteristics,reinforcing the pathogenicity of BRF1 gene mutations and expanding the manifestation spectrum of CFDS. | Xin Zhao Yan Lan Jinfeng Miao Guo Li Wenzhe Sun Xiuli Qiu Suiqiang Zhu Zhou Zhu | 2022 | Chinese Medical Journal2022，135，19： | 0 |
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